Poland's syndrome and spontaneous pneumothorax a rare association

Çelik B.

TUBERKULOZ VE TORAK-TUBERCULOSIS AND THORAX, vol.58, no.2, pp.173-176, 2010 (ESCI) identifier identifier identifier

  • Publication Type: Article / Article
  • Volume: 58 Issue: 2
  • Publication Date: 2010
  • Journal Name: TUBERKULOZ VE TORAK-TUBERCULOSIS AND THORAX
  • Journal Indexes: Emerging Sources Citation Index (ESCI), Scopus, TR DİZİN (ULAKBİM)
  • Page Numbers: pp.173-176
  • Keywords: Poland syndrome, pneumothorax, spontaneous, anomaly
  • Ondokuz Mayıs University Affiliated: Yes

Abstract

Poland's syndrome is an uncommon congenital anomaly characterized by unilateral absence of pectoralis major muscle, ipsilateral hand abnormalities, and a variety of associated anomalies. The incidence of the syndrome ranges from 1/7000 to 1/100.000. The syndrome is observed more frequently in man than in woman. A 22-years-old man who was admitted with a history of chest pain and dyspnea to our emergency department. On examination, breath sounds were decreased on the right side, there was an absence of the pectoralis major muscle, a shortness on the right upper limb and a restriction on the right shoulder and right elbow. Initially chest radiograph showed total pneumothorax on the right side. The patient was treated with tube thoracostomy. This case is presented to draw attention to the association of Poland syndrome with spontaneous pneumothorax.