Research Information System
KSDF 2024 - Kadın Sağlığı Dernekleri Federasyonu Kongresi, Antalya, Turkey, 17 - 21 April 2024, pp.118, (Full Text)
INTRODUCTION: Subdiaphragmatic extralobar pulmonary sequestration is a rare type of pulmonary sequestration that is often discovered incidentally during routine ultrasound scans. Its prevalence has increased as equipment resolution has improved, awareness of perinatologists, and radiologists has increased. This study reported on a fetus diagnosed with supradiaphragmatic and subdiaphragmatic pulmonary sequestration via prenatal ultrasound.
CASE: A 25-year-old G1 mother with a gestational age of 16 weeks and 6 days, presented to the perinatology clinic from an external center due to an increase in nuchal translucency. The patient had no significant medical history or genetic predisposition within the family. In the ultrasound evaluation, there was a lesion at the base of the left lung, measuring 20*22*16 mm, with a supradiaphragmatic wedge-shaped hyperechoic appearance. It is receiving circulation from the descending aorta on Doppler examination. Adjacent to the mass, an extrathoracic subdiaphragmatic mass measuring 10*8*9 mm was observed. The lesions were consistent with bronchopulmonary sequestration. Amniocentesis was performed and microarray result was normal. Serial prenatal follow-up ultrasound examinations were performed to evaluate the change in the size of the lung mass and the development of hydrops. Hydrops did not develop and the size of the mass regressed during follow-up.
DISCUSSION: Bronchopulmonary sequestration is classified as intralobar and extralobar according to its structure and venous drainage. Extralobar sequestration (ELS) lack connection with the tracheobronchial system and can be supradiaphragmatic, subdiaphragmatic, or transdiaphragmatic. ELS is predominantly supradiaphragmatic (85-90%) and typically located on the left. It is important to differentiate subdiaphragmatic cases of ELS from adrenal gland pathologies. O Close monitoring is necessary to observe the development of hydrops or pleural effusion. Spontaneous resolution is possible. Typically, no treatment is administered during the prenatal period, but in the presence of hydrops, options include laser coagulation, steroids, and either birth or thoracoamniotic shunt.