Bilateral adrenal cystic neuroblastoma with superior vena cava syndrome and massive intracystic haemorrhage

Pinarli F., Danaci M., TANDER B., Dagdemir A., Diren B., Acar S., ...More

PEDIATRIC RADIOLOGY, vol.34, no.9, pp.746-749, 2004 (SCI-Expanded) identifier

  • Publication Type: Article / Article
  • Volume: 34 Issue: 9
  • Publication Date: 2004
  • Doi Number: 10.1007/s00247-004-1209-5
  • Journal Name: PEDIATRIC RADIOLOGY
  • Journal Indexes: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Page Numbers: pp.746-749
  • Keywords: adrenal neuroblastoma, cyst, haemorrhage, superior vena cava syndrome, ultrasound, CT, child, NEURO-BLASTOMA, FEATURES, HEMOPERITONEUM, CHILDHOOD
  • Ondokuz Mayıs University Affiliated: No

Abstract

Bilateral cystic adrenal tumours are a rare presentation of neuroblastoma. Intratumoural haemorrhage is a frequent finding in neuroblastoma, but is rarely symptomatic. We present an 11-month-old girl with predominantly cystic bilateral neuroblastomas and distant lymph-node metastasis. Massive intracystic haemorrhage and superior vena cava (SVC) syndrome were ominous prognostic factors, leading to death. Large tumours with intracystic haemorrhage might require a conservative approach.