Intrathoracic malignant peripheral nerve sheath tumor with angtosarcoma in a child with NF1

Elli, Murat; Can Meydan, Bilge; Ceyhan, Meltem; Pinarli, Faruk; Dağdemir, Ayhan; Ayyildiz, Halil; Guersell, Bilge; Dagcinar, Adnan

Intrathoracic malignant peripheral nerve sheath tumor with angtosarcoma in a child with NF1

Elli M., Can Meydan B., Ceyhan M., Pinarli F. G., Dağdemir A., Ayyildiz H. S., ...More

TUMORI JOURNAL, vol.93, no.6, pp.641-644, 2007 (SCI-Expanded, Scopus)

Publication Type: Article / Article
Volume: 93 Issue: 6
Publication Date: 2007
Journal Name: TUMORI JOURNAL
Journal Indexes: Science Citation Index Expanded (SCI-EXPANDED), Scopus
Page Numbers: pp.641-644
Keywords: angiosarcoma, childhood, malignant peripheral nerve sheath tumors, NF1, VASCULAR TUMORS, ANGIOSARCOMA, SARCOMA, ADOLESCENTS, BENIGN
Ondokuz Mayıs University Affiliated: Yes

Abstract

Malignant peripheral nerve sheath tumors (MPNSTs) are uncommon in children and adolescents but occur more frequently in NF1 patients. Angiosarcomatous differentiation in MPNSTs is a rare entity with poor prognosis. We report on a 13-year-old boy with intrathoracic angiosarcoma arising in MPNST associated with NF1.