A case of Prune-belly syndrome associated with multiple congenital anomalies Multipl konjenital anomalilerin eslik ettigi bir Prune-belly sendromu olgusu


Yıldız L., Aydin O., Boran C., Kandemir B., Alper T.

Ondokuz Mayis Universitesi Tip Dergisi, vol.15, no.4, pp.330-334, 1998 (Scopus) identifier

  • Publication Type: Article / Article
  • Volume: 15 Issue: 4
  • Publication Date: 1998
  • Journal Name: Ondokuz Mayis Universitesi Tip Dergisi
  • Journal Indexes: Scopus, TR DİZİN (ULAKBİM)
  • Page Numbers: pp.330-334
  • Keywords: Multiple congenital anomalies, Prune-belly syndrome
  • Ondokuz Mayıs University Affiliated: Yes

Abstract

Abdominal muscle deficiency, urinary tract abnormalities and cryptoorchidism are the three major features of the Prune-belly syndrome. Massive acites and intraabdominal urine accumination had produced abdominal wall atrophy. A functional or anatomic urethral obstruction may detect on cases. As an addition classic triad of Prune-belly syndrome our case has polydactily, cleft lip and palate. Chromosomal analysis could not be done our cases due to in utero exitus.